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Evidence that oxidative stress is increased in patients with X-linked adrenoleukodystrophy
British Library Online Contents | 2004| -
Glutaric acid moderately compromises energy metabolism in rat brain
British Library Online Contents | 2005| -
Alanine Prevents the Inhibition of Pyruvate Kinase Activity Caused by Tryptophan in Cerebral Cortex of Rats
British Library Online Contents | 2003| -
l-Carnitine Blood Levels and Oxidative Stress in Treated Phenylketonuric Patients
British Library Online Contents | 2009| -
Oxidative stress parameters in diabetic rats submitted to forced swimming test: the clonazepam effect
British Library Online Contents | 2007| -
Setting up a laboratory for organic acidaemias detection in developing country: is that worthwhile?
British Library Conference Proceedings | 1994| -
Using gas and liquid chromatography for the biochemical diagnosis of aminoacidopathies and organic acidaemias
British Library Online Contents | 1997| -
Progression rate of myelopathy in X-linked adrenoleukodystrophy heterozygotes
British Library Online Contents | 2015| -
Induction of Oxidative Stress by Chronic and Acute Glutaric Acid Administration to Rats
British Library Online Contents | 2007| -
l-Carnitine supplementation decreases DNA damage in treated MSUD patients
British Library Online Contents | 2015| -
Investigation of inflammatory profile in MSUD patients: benefit of L-carnitine supplementation
British Library Online Contents | 2015| -
Energy Metabolism is Compromised in Skeletal Muscle of Rats Chronically-Treated with Glutaric Acid
British Library Online Contents | 2007| -
Oxidative stress in patients with mucopolysaccharidosis type II before and during enzyme replacement therapy
British Library Online Contents | 2011| -
167-P 3-Hydroxy-3-methylglutaric aciduria: report of 15 Brazilian patients
British Library Conference Proceedings | 2007| -
Reduction of large neutral amino acid levels in plasma and brain of hyperleucinemic rats
British Library Online Contents | 2001|