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  1.  

    Mice lacking caspase-2 are protected from behavioral changes, but not pathology, in the YAC128 model of Huntington disease

    Free access
    Carroll, Jeffrey B / Southwell, Amber L / Graham, Rona K et al. | BASE | 2011
    Keywords: Huntington’s Disease
  2.  

    Effects of Pin1 Loss in HdhQ111 Knock-in Mice

    Free access
    Agostoni, Elena / Michelazzi, Silvia / Maurutto, Marta et al. | BASE | 2016
    Keywords: Huntington’s disease
  3.  

    Similar striatal gene expression profiles in the striatum of the YAC128 and HdhQ150 mouse models of Huntington's disease are not reflected in mutant Huntingtin inclusion prevalence

    Free access
    Bayram-Weston, Z / Stone, TC / Giles, P et al. | BASE | 2015
    Keywords: Huntington's disease; Neurodegeneration; Gene expression; Transgenic mouse models; Behaviour
  4.  

    Adult Neural Stem Cell Proliferation is Not Altered in Transgenic Mice Over-expressing BDNF or Mutant Huntingtin in Forebrain

    Free access
    Bahga, Dalbir / Guthrie, Kathleen | BASE | 2012
    Keywords: neural stem cell proliferation; htt; Huntington's Disease; BDNF; SVZ
  5.  

    Deimmunization for gene therapy: host matching of synthetic zinc finger constructs enables long-term mutant Huntingtin repression in mice

    Free access
    Agustín Pavón, Carmen / Mielcarek, Michael / Isalan, Mark et al. | BASE
    Keywords: Monogenetic disease, Huntington’s disease
  6.  

    Modulation of Mutant Huntingtin N-Terminal Cleavage and Its Effect on Aggregation and Cell Death

    Free access
    Juenemann, Katrin / Weisse, Christina / Reichmann, Denise et al. | BASE | 2010
    Keywords: Huntington’s disease – Huntingtin – Polyglutamine – Proteolytic processing – N-terminal fragment
  7.  

    Conditional targeting of medium spiny neurons in the striatal matrix

    Free access
    Reinius, Björn / Blunder, Martina / Brett, Frances M. et al. | BASE | 2015
    Keywords: huntington's disease
  8.  

    Modulation of Huntingtin Toxicity by BAG1 is Dependent on an Intact BAG Domain

    Free access
    Liman, Jan / Sroka, Kamila / Dohm, Christoph P. et al. | BASE
    Keywords: BAG1; Huntington’s disease; Chaperone system; Siah1
  9.  

    Conditional targeting of medium spiny neurons in the striatal matrix

    Free access
    Reinius, Björn / Blunder, Martina / Brett, Frances M. et al. | BASE | 2015
    Keywords: huntington's disease
  10.  

    Recombinant adeno associated viral (AAV) vector type 9 delivery of Ex1-Q138-mutant huntingtin in the rat striatum as a short-time model for in vivo studies in drug discovery

    Free access
    Ceccarelli, Ilaria / Fiengo, Pasquale / Remelli, Rosaria et al. | BASE | 2016
    Keywords: Huntington's disease
  11.  

    Acyl CoA Binding Domain Containing 3 (ACBD3) Protein in Huntington’s Disease Human Skin Fibroblasts

    Free access
    Kratochvílová, H. / Rodinová, M. / Sládková, J. et al. | BASE | 2015
    Keywords: Huntington’s disease
  12.  

    Reduced hippocampal neurogenesis in R6/2 transgenic Huntington's disease mice

    Free access
    Gil, Joana M. A. C. / Mohapel, Paul / Araújo, Inês M. et al. | BASE | 2005
    Keywords: Huntington's disease
  13.  

    Long-term lentiviral-mediated expression of ciliary neurotrophic factor in the striatum of Huntington's disease transgenic mice

    Free access
    Zala, Diana / Bensadoun, Jean-Charles / Pereira de Almeida, Luis et al. | BASE | 2004
    Keywords: Huntington's disease
  14.  

    Polyglutamine tracts regulate beclin 1-dependent autophagy

    Ashkenazi, Avraham / Bento, Carla F / Ricketts, Thomas et al. | Online Contents | 2017
    Keywords: Huntington's chorea, Huntington's disease, Huntingtons disease, Machado-Joseph disease
  15.  

    Metabolic signatures of Huntington's disease (HD): 1 H NMR analysis of the polar metabolome in post-mortem human brain

    Free access
    Graham, Stewart F. / Kumar, Praveen K. / Bjorndahl, Trent et al. | BASE | 2016
    Keywords: Huntington's disease
  16.  

    Structure of a single-chain Fv bound to the 17 N-terminal residues of huntingtin provides insights into pathogenic amyloid formation and suppression

    De Genst, Erwin / Chirgadze, Dimitri Y / Klein, Fabrice A C et al. | Online Contents | 2015
    Keywords: Huntington's disease, HD, Huntington's disease
  17.  

    Prefibrillar huntingtin oligomers isolated from HD brain potently seed amyloid formation

    Morozova, Olga A / Gupta, Sharad / Colby, David W | Online Contents | 2015
    Keywords: Huntington's disease, Huntington Disease - metabolism

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