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099-A Oxidative stress in maple syrup urine disease: antioxidant enzyme activities and selenium levels
British Library Conference Proceedings | 2007| -
123-P Increased incidence of 3-hydroxy-3-methylglutaric aciduria in Brazil
British Library Online Contents | 2001| -
144-P Evidence that glutaric and 3-hydroxyglutaric acids act synergistically disturbing energy metabolism in rat brain cortex
British Library Conference Proceedings | 2007| -
167-P 3-Hydroxy-3-methylglutaric aciduria: report of 15 Brazilian patients
British Library Conference Proceedings | 2007| -
A chemically-induced acute model of maple syrup urine disease in rats for neurochemical studies
British Library Online Contents | 2006| -
Alanine Prevents the Inhibition of Pyruvate Kinase Activity Caused by Tryptophan in Cerebral Cortex of Rats
British Library Online Contents | 2003| -
Amino acids levels and lipid peroxidation in maple syrup urine disease patients
British Library Online Contents | 2009| -
Biomolecules damage and redox status abnormalities in Fabry patients before and during enzyme replacement therapy
British Library Online Contents | 2016| -
Brain effect of insulin and clonazepam in diabetic rats under depressive-like behavior
British Library Online Contents | 2013| -
Concurrent folate treatment prevents Na+,K+-ATPase activity inhibition and memory impairments caused by chronic hyperhomocysteinemia during rat development
British Library Online Contents | 2007| -
D-2-Hydroxyglutaric aciduria in a patient with a severe clinical phenotype and unusual MRI findings
British Library Online Contents | 2001| -
Development of an animal model for chronic mild hyperhomocysteinemia and its response to oxidative damage
British Library Online Contents | 2011| -
Disturbance of redox homeostasis as a contributing underlying pathomechanism of brain and liver alterations in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency
British Library Online Contents | 2015| -
Dual mechanism of brain damage induced in vivo by the major metabolites accumulating in hyperornithinemia-hyperammonemia-homocitrullinuria syndrome
British Library Online Contents | 2011| -
Early biochemical effects after unilateral hypoxia–ischemia in the immature rat brain
British Library Online Contents | 2011| -
Effect of In Vivo Administration of Ethylmalonic Acid on Energy Metabolism in Rat Tissues
British Library Online Contents | 2006|