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013-P Glycine induces lipid oxidative damage and reduces the antioxidant defenses in brain cortex of young rats
British Library Conference Proceedings | 2008| -
099-A Oxidative stress in maple syrup urine disease: antioxidant enzyme activities and selenium levels
British Library Conference Proceedings | 2007| -
123-P Increased incidence of 3-hydroxy-3-methylglutaric aciduria in Brazil
British Library Online Contents | 2001| -
167-P 3-Hydroxy-3-methylglutaric aciduria: report of 15 Brazilian patients
British Library Conference Proceedings | 2007| -
A chemically-induced acute model of maple syrup urine disease in rats for neurochemical studies
British Library Online Contents | 2006| -
Alanine Prevents the Inhibition of Pyruvate Kinase Activity Caused by Tryptophan in Cerebral Cortex of Rats
British Library Online Contents | 2003| -
Amino acids levels and lipid peroxidation in maple syrup urine disease patients
British Library Online Contents | 2009| -
Chronic administration of propionic acid reduces ganglioside N-acetylneuraminic acid concentration in cerebellum of young rats
British Library Online Contents | 1998| -
D-2-Hydroxyglutaric aciduria in a patient with a severe clinical phenotype and unusual MRI findings
British Library Online Contents | 2001| -
Disturbance of redox homeostasis as a contributing underlying pathomechanism of brain and liver alterations in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency
British Library Online Contents | 2015| -
Effect of Chemically Induced Propionic Acidemia on Neurobehavioral Development of Rats - A critical review
British Library Online Contents | 1999| -
Effect of In Vivo Administration of Ethylmalonic Acid on Energy Metabolism in Rat Tissues
British Library Online Contents | 2006| -
Effect of short- and long-term exposition to high phenylalanine blood levels on oxidative damage in phenylketonuric patients
British Library Online Contents | 2009| -
Energy Metabolism is Compromised in Skeletal Muscle of Rats Chronically-Treated with Glutaric Acid
British Library Online Contents | 2007| -
Erythrocyte glutathione peroxidase activity and plasma selenium concentration are reduced in maple syrup urine disease patients during treatment
British Library Online Contents | 2007| -
Evidence that oxidative stress is increased in plasma from patients with maple syrup urine disease
British Library Online Contents | 2006| -
Experimental Evidence that Phenylalanine Provokes Oxidative Stress in Hippocampus and Cerebral Cortex of Developing Rats
British Library Online Contents | 2010| -
Experimental evidence that pristanic acid disrupts mitochondrial homeostasis in brain of young rats
British Library Online Contents | 2012| -
Glutaric acid moderately compromises energy metabolism in rat brain
British Library Online Contents | 2005| -
Guanosine Enhances Glutamate Uptake in Brain Cortical Slices at Normal and Excitotoxic Conditions
British Library Online Contents | 2002| -
Increased incidence of 3-hydroxy-3-methylglutaric aciduria in Brazil
British Library Conference Proceedings | 2001| -
Induction of lipid peroxidation and decrease of antioxidant defenses in symptomatic and asymptomatic patients with X-linked adrenoleukodystrophy
British Library Online Contents | 2007| -
Induction of Oxidative Stress by Chronic and Acute Glutaric Acid Administration to Rats
British Library Online Contents | 2007| -
Inhibition of Na+,K+-ATPase activity in synaptosomes from cerebral cortex of young rats by 3-methylglutaric acid
British Library Online Contents | 2010| -
Inhibition of Na+,K+-ATPase activity in synaptosomes from cerebral cortex of young rats by 3-methylglutaric acid
British Library Conference Proceedings | 2010| -
Investigation of inflammatory profile in MSUD patients: benefit of L-carnitine supplementation
British Library Online Contents | 2015| -
Investigation of oxidative stress parameters in treated phenylketonuric patients
British Library Online Contents | 2006| -
In vitro evidence that phytanic acid compromises Na^+,K^+-ATPase activity and the electron flow through the respiratory chain in brain cortex from young rats
British Library Online Contents | 2010| -
l-Carnitine Blood Levels and Oxidative Stress in Treated Phenylketonuric Patients
British Library Online Contents | 2009| -
Lipoperoxidation in patients with disorders of propionate metabolism is prevented by treatment with L-carnitine
British Library Online Contents | 2010| -
Lipoperoxidation in patients with disorders of propionate metabolism is prevented by treatment with L-carnitine
British Library Conference Proceedings | 2010| -
Lower in vivo brain extracellular GABA concentration in diabetic rats during forced swimming
British Library Online Contents | 2003| -
Low plasma levels of phenylalanine, tyrosine, tryptophan and methionine in maple syrup urine disease patients during crisis
British Library Online Contents | 1998| -
Lysine induces lipid and protein damage and decreases reduced glutathione concentrations in brain of young rats
British Library Online Contents | 2008| -
Maple syrup urine disease in treated patients: Biochemical and oxidative stress profiles
British Library Online Contents | 2008| -
Osmoprotection by compatible solutes accumulation in the moderately halophilic bacterium Halomonas elongata DSM 3043
British Library Online Contents | 2000| -
Oxidative stress in Niemann-Pick type C patients: a protective role of N-butyl-deoxynojirimycin therapy
British Library Online Contents | 2012| -
Oxidative Stress in Patients with X-Linked Adrenoleukodystrophy
British Library Online Contents | 2016| -
Oxidative stress in plasma from maple syrup urine disease patients during treatment
British Library Online Contents | 2008| -
Oxidative Stress Parameters in Urine from Patients with Disorders of Propionate Metabolism: a Beneficial Effect of l-Carnitine Supplementation
British Library Online Contents | 2012| -
Phytanic acid induces oxidative stress in cerebellum and cerebral cortex of young rats
British Library Online Contents | 2010| -
Phytanic acid induces oxidative stress in cerebellum and cerebral cortex of young rats
British Library Conference Proceedings | 2010| -
Pristanic acid promotes oxidative stress in brain cortex of young rats: A possible pathophysiological mechanism for brain damage in peroxisomal disorders
British Library Online Contents | 2011|