Cytotoxic CD8 + T lymphocytes expressing ALS-causing SOD1 mutant selectively trigger death of spinal motoneurons. (English)
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Title:Cytotoxic CD8 + T lymphocytes expressing ALS-causing SOD1 mutant selectively trigger death of spinal motoneurons.
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Contributors:Coque, E. ( author ) / Salsac, C. ( author ) / Espinosa-Carrasco, G. ( author ) / Varga, B. ( author ) / Degauque, N. ( author ) / Cadoux, M. ( author ) / Crabé, R. ( author ) / Virenque, A. ( author ) / Soulard, C. ( author ) / Fierle, J.K. ( author )
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Publication date:2019-02-05
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Remarks:Proceedings of the National Academy of Sciences of the United States of America, vol. 116, no. 6, pp. 2312-2317
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DOI:
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Type of media:Article (Journal)
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Type of material:Electronic Resource
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Language:English
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Keywords:Amyotrophic Lateral Sclerosis/diagnosis , Amyotrophic Lateral Sclerosis/genetics , Amyotrophic Lateral Sclerosis/metabolism , Amyotrophic Lateral Sclerosis/physiopathology , Animals , Cell Communication/immunology , Cell Death , Cell Survival/genetics , Disease Models , Animal , Gene Expression , Granzymes/metabolism , Histocompatibility Antigens Class I/immunology , Lymphocyte Activation/immunology , Mice , Transgenic , Motor Neurons/immunology , Motor Neurons/metabolism , Mutation , Phenotype , Severity of Illness Index , Spinal Cord/cytology , Superoxide Dismutase-1/genetics , T-Lymphocytes , Cytotoxic/immunology , Cytotoxic/metabolism , fas Receptor/metabolism , amyotrophic lateral sclerosis , cytotoxic T lymphocytes , major histocompatibility complex I , motoneuron , neuroimmunity
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